Orthokeratinized Odontogenic Cyst: A case report with Clinicopathological review

Orthokeratinized Odontogenic Cyst (OOC) is a developmental cyst of odontogenic origin of jaw, which was formerly considered by the World Health Organization (WHO) as the uncommon orthokeratinized variant of Odontogenic Keratocyst (OKC), until the WHO in 2005, where it was separated from the Keratocystic Odontogenic Tumor (KCOT). It is an uncommon developmental cyst comprising of 0.4% of all odontogenic cyst and shows peculiar clinicopathologic aspects when compared with other developmental odontogenic lesions such as Dentigerous cyst and the Keratocystic Odontogenic Tumor. Clinically, it occurs as a solitary cyst, shows predilection for males and most often found in second to fifth decade. It mainly occurs in mandible, least recurrence was noted after surgical removal of the lesion. The purpose of this article is to present a case of OOC arising in the mandible and to discuss the review of literature.